Derechos | Preview | Fecha Public. | Título | Autor(es) | Tipo |
openAccess | | dic-2023 | Actin Polymerization Defects Induce Mitochondrial Dysfunction in Cellular Models of Nemaline Myopathies | Piñero-Perez, Rocío; López-Cabrera, Alejandra; Álvarez-Córdoba, Mónica; Cilleros-Holgado, Paula; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Gómez-Fernández, David; Reche-López, Diana; Romero-González, Ana; Romero-Domínguez, José Manuel; Pablos, Rocío M. de; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 2022 | Activation of the mitochondrial unfolded protein response: A new therapeutic target? | Suarez-Rivero, Juan M. CSIC ORCID; Pastor-Maldonado, Carmen J.; Povea-Cabello, Suleva; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 13-abr-2023 | Additional file 1 of Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels [Dataset] | Talaverón-Rey, Marta; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Povea-Cabello, Suleva; Suarez-Rivero, Juan M. CSIC ORCID; Gómez-Fernández, David; Romero-González, Ana; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Cilleros-Holgado, Paula; Reche-López, Diana; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | dataset |
openAccess | | 2023 | Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels | Talaverón-Rey, Marta; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Povea-Cabello, Suleva; Suarez-Rivero, Juan M. CSIC ORCID; Gómez-Fernández, David; Romero-González, Ana; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Cilleros-Holgado, Paula; Reche-López, Diana; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 1-oct-2023 | Antioxidants Prevent Iron Accumulation and Lipid Peroxidation, but Do Not Correct Autophagy Dysfunction or Mitochondrial Bioenergetics in Cellular Models of BPAN | Suárez-Carrillo, Alejandra; Álvarez-Córdoba, Mónica; Romero-González, Ana; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Cilleros-Holgado, Paula; Piñero-Perez, Rocío; Reche-López, Diana; Gómez-Fernández, David; Romero-Domínguez, José Manuel; Munuera, Manuel CSIC; Díaz, Antonio; González-Granero, Susana; García-Verdugo, José Manuel; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 2023 | Mitochondrial Quality Control via Mitochondrial Unfolded Protein Response (mtUPR) in Ageing and Neurodegenerative Diseases | Cilleros-Holgado, Paula; Gómez-Fernández, David; Piñero-Perez, Rocío; Romero-Domínguez, José Manuel; Reche-López, Diana; López-Cabrera, Alejandra; Álvarez-Córdoba, Mónica; Munuera, Manuel CSIC; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Romero-González, Ana; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 2023 | mtUPR Modulation as a Therapeutic Target for Primary and Secondary Mitochondrial Diseases | Cilleros-Holgado, Paula; Gómez-Fernández, David; Piñero-Perez, Rocío; Reche-López, Diana; Álvarez-Córdoba, Mónica; Munuera, Manuel CSIC; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Suárez-Carrillo, Alejandra; Romero-González, Ana; Suarez-Rivero, Juan M. CSIC ORCID; Romero-Domínguez, José Manuel; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo de revisión |
openAccess | | 2023 | Neurodegeneration, Mitochondria, and Antibiotics | Suarez-Rivero, Juan M. CSIC ORCID; López-Pérez, Juan; Muela-Zarzuela, Inés; Pastor-Maldonado, Carmen J.; Cilleros-Holgado, Paula; Gómez-Fernández, David; Álvarez-Córdoba, Mónica; Munuera, Manuel CSIC; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Suárez-Carrillo, Alejandra; Piñero-Perez, Rocío; Reche-López, Diana; Romero-Domínguez, José Manuel; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo de revisión |
openAccess | | 2022 | Pantothenate and L-Carnitine supplementation improves pathological alterations in cellular models of KAT6A syndrome | Munuera, Manuel CSIC; Álvarez-Córdoba, Mónica; Suarez-Rivero, Juan M. CSIC ORCID; Povea-Cabello, Suleva; Villalón-García, Irene; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
| | 2023 | Patient-Derived Cellular Models for Polytarget Precision Medicine in Pantothenate Kinase-Associated Neurodegeneration | Álvarez-Córdoba, Mónica; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Cilleros-Holgado, Paula; Gómez-Fernández, David; Piñero-Perez, Rocío; Reche-López, Diana; Munuera, Manuel CSIC; Suárez-Carrillo, Alejandra; Romero-González, Ana; Romero-Domínguez, José Manuel; López-Cabrera, Alejandra; Armengol, José Ángel; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo de revisión |
openAccess | | 2022 | Therapeutic approach with commercial supplements for pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels | Álvarez-Córdoba, Mónica; Reche-López, Diana; Cilleros-Holgado, Paula; Talaverón-Rey, Marta; Villalón-García, Irene; Povea-Cabello, Suleva; Suarez-Rivero, Juan M. CSIC ORCID; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 2022 | UPRmt activation improves pathological alterations in cellular models of mitochondrial diseases | Suarez-Rivero, Juan M. CSIC ORCID; Pastor-Maldonado, Carmen J.; Povea-Cabello, Suleva; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | jun-2023 | Vicious cycle of lipid peroxidation and iron accumulation in neurodegeneration | Villalón-García, Irene; Povea-Cabello, Suleva; Álvarez-Córdoba, Mónica; Talaverón-Rey, Marta; Suarez-Rivero, Juan M. CSIC ORCID; Suárez-Carrillo, Alejandra; Munuera, Manuel CSIC; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Perez, Rocío; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo de revisión |