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Derechos | Preview | Fecha Public. | Título | Autor(es) | Tipo |
closedAccess | | 2012 | Defects in mTR stability and telomerase activity produced by the Dkc1 A353V mutation in dyskeratosis congenita are rescued by a peptide from the dyskerin TruB domain | Machado-Pinilla, R. CSIC; Carrillo, Jaime CSIC; Manguan-García, Cristina CSIC ORCID; Sastre, Leandro CSIC ORCID; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2014 | Development and validation of a rapid HPLC method for the quantification of GSE4 peptide in biodegradable PEI-PLGA nanoparticles | Egusquiaguirre, Susana P.; Manguan-García, Cristina CSIC ORCID; Perona Abellón, Rosario CSIC ORCID; Igartua, Manuela | artículo |
closedAccess | | 2015 | Development of surface modified biodegradable polymeric nanoparticles to deliver GSE24.2 peptide to cells: A promising approach for the treatment of defective telomerase disorders | Egusquiaguirre, Susana P.; Manguan-García, Cristina CSIC ORCID; Pintado-Berninches, Laura CSIC ORCID ; Perona Abellón, Rosario CSIC ORCID; Igartua, Manuela | artículo |
openAccess | | 2019 | Dyskeratosis Congenita | Perona Abellón, Rosario CSIC ORCID; Manguan-García, Cristina CSIC ORCID; Sastre, Leandro CSIC ORCID | capítulo de libro |
openAccess | | 2014 | Expression of the genetic suppressor element 24.2 (GSE24.2) decreases DNA damage and oxidative stress in X-linked dyskeratosis congenita cells | Manguan-García, Cristina CSIC ORCID; Pintado-Berninches, Laura CSIC ORCID ; Carrillo, Jaime CSIC; Machado-Pinilla, R. CSIC; Sastre, Leandro CSIC ORCID; Pallardó, Federico V.; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2004 | FK506 sensitizes mammalian cells to high osmolarity by modulating p38 MAP kinase activation | Sánchez-Pérez, Isabel CSIC ORCID; Manguan-García, Cristina CSIC ORCID; Perona Abellón, Rosario CSIC ORCID; Murguía, José Ramón CSIC ORCID | artículo |
openAccess | | 2018 | Generation and potential applications of an X-linked dyskeratosis congenita model in human hematopoietic stem cells | Carrascoso-Rubio, C. CSIC; Zittersteijn, H. A.; Pintado-Berninches, Laura CSIC ORCID ; Fernández-Varas, Beatriz CSIC; Lozano, M. L.; Manguan-García, Cristina CSIC ORCID; Sastre, Leandro CSIC ORCID; Bueren-Calabuig, Juan A.; Perona Abellón, Rosario CSIC ORCID; Guenechea, Guillermo | comunicación de congreso |
openAccess | | 2021 | Generation of dyskeratosis congenita-like hematopoietic stem cells through the stable inhibition of DKC1 | Carrascoso-Rubio, C. CSIC; Zittersteijn, H. A.; Pintado-Berninches, Laura CSIC ORCID ; Fernández-Varas, Beatriz CSIC; Lozano, M. L.; Manguan-García, Cristina CSIC ORCID; Sastre, Leandro CSIC ORCID; Bueren-Calabuig, Juan A.; Perona Abellón, Rosario CSIC ORCID; Guenechea, Guillermo | artículo |
closedAccess | | 22-ene-2019 | GSE4 peptide suppresses oxidative and telomere deficiencies in Ataxia Telangiectasia patient cells | Pintado-Berninches, Laura CSIC ORCID ; Fernández-Varas, Beatriz CSIC; Benitez-Buelga, Carlos CSIC; Manguan-García, Cristina CSIC ORCID; Serrano-Benítez, Almudena CSIC; Iarriccio, Laura; Carrillo, Jaime CSIC; Guenechea, Guillermo; Egusquiaguirre, Susana P.; Pedraz, José Luís; Hernández, Rosa M.; Igartua, Manuela; Arias-Salgado, Elena G.; Cortés-Ledesma, Felipe CSIC ORCID; Sastre, Leandro CSIC ORCID; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2015 | GSE4 reverts fibrosis in bleomycin treated rats with Idipathic pulmonary fibrosis | Cortijo, Julio; Manguan-García, Cristina CSIC ORCID; Pintado-Berninches, Laura CSIC ORCID ; Sastre, Leandro CSIC ORCID; Egusquiaguirre, Susana P.; Igartua, Manuela; Perona Abellón, Rosario CSIC ORCID | comunicación de congreso |
openAccess | | 2015 | GSE4, a small dyskerin- and GSE24.2-related peptide, induces telomerase activity, cell proliferation and reduces DNA damage, oxidative stress and cell senescence in dyskerin mutant cells | Iarriccio, Laura; Manguan-García, Cristina CSIC ORCID; Pintado-Berninches, Laura CSIC ORCID ; Mancheño, Jose M. CSIC ORCID; Molina, A.; Perona Abellón, Rosario CSIC ORCID; Sastre, Leandro CSIC ORCID | artículo |
closedAccess | | 2015 | GSE4, a small dyskerin- and GSE24.2-related peptide, induces telomerase and c-myc expression and reduces DNA damage and oxidative stress in dyskerin mutant cells | Iarriccio, Laura; Manguan-García, Cristina CSIC ORCID; Mancheño, Jose M. CSIC ORCID; Pintado-Berninches, Laura CSIC ORCID ; Molina, A.; Perona Abellón, Rosario CSIC ORCID; Sastre, Leandro CSIC ORCID | póster de congreso |
openAccess | | mar-2021 | GSE4-loaded nanoparticles a potential therapy for lung fibrosis that enhances pneumocyte growth, reduces apoptosis and DNA damage | Pintado-Berninches, Laura CSIC ORCID ; Montes-Worboys, Ana; Manguan-García, Cristina CSIC ORCID; Arias-Salgado, Elena G.; Serrano, Adela; Fernández-Varas, Beatriz CSIC; Guerrero-López, Rosa CSIC; Iarriccio, Laura; Planas-Cerezales, Lurdes; Guenechea, Guillermo; Egusquiaguirre, Susana P.; Hernández, Rosa M.; Igartua, Manuela; Pedraz, José Luís; Cortijo, Julio; Sastre, Leandro CSIC ORCID; Molina-Molina, María; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2009 | hCCR4/cNOT6 targets DNA-damage response proteins | Sánchez-Pérez, Isabel CSIC ORCID; Manguan-García, Cristina CSIC ORCID; Menacho-Márquez, Mauricio CSIC ORCID; Murguía, José Ramón CSIC ORCID; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2012 | High resolution melting analysis for the identification of novel mutations in DKC1 and TERT genes in patients with dyskeratosis congenita | Carrillo, Jaime CSIC; Moratilla, Carmen CSIC; González, A.; Manguan-García, Cristina CSIC ORCID; Sastre, Leandro CSIC ORCID; Perona Abellón, Rosario CSIC ORCID | artículo |
openAccess | | 4-abr-2014 | Liberación de sustancias en células senescentes | Martínez Máñez, Ramón; Murguía, José Ramón CSIC ORCID; Perona Abellón, Rosario CSIC ORCID; Agostini, Alessandro; Mondragón Martínez, Laura; Moreno Torres, Marta CSIC; Manguan-García, Cristina CSIC ORCID; Marcos, M. Dolores; Soto, Joan; Sancenón, Félix | solicitud de patente |
openAccess | | 4-abr-2014 | Liberación de sustancias en células senescentes | Martínez Máñez, Ramón; Murguía, José Ramón CSIC ORCID; Perona Abellón, Rosario CSIC ORCID; Agostini, Alessandro; Mondragón Martínez, Laura; Moreno Torres, Marta CSIC; Manguan-García, Cristina CSIC ORCID; Marcos, M. Dolores; Soto, Joan; Sancenón, Félix | patente |
closedAccess | | 2009 | MKP1 repression is required for the chemosensitizing effects of NF-κB and PI3K inhibitors to cisplatin in non-small cell lung cancer | Cortés-Sempere, María CSIC; Rodriguez-Fanjul, V. CSIC ORCID; Belda-Iniesta, Cristobal; Cejas, Paloma; Machado-Pinilla, R. CSIC; Manguan-García, Cristina CSIC ORCID; Sánchez-Pérez, Isabel CSIC ORCID; Nistal, Manuel; Moratilla, Carmen CSIC; Castro Carpeño, Javier de; González Barón, Manuel; Albanell, Joan; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2006 | MKP1/CL100 controls tumor growth and sensitivity to cisplatin in non-small-cell lung cancer | Chattopadhyay, S.; Machado-Pinilla, R. CSIC; Manguan-García, Cristina CSIC ORCID; Belda-Iniesta, Cristobal; Moratilla, Carmen CSIC; Fresno Vara, Juan Ángel CSIC; Castro Carpeño, Javier de; Casado, Enrique CSIC; Nistal, Manuel; González Barón, Manuel; Perona Abellón, Rosario CSIC ORCID | artículo |
closedAccess | | 2017 | Mutations in XLF/NHEJ1/Cernunnos gene results in downregulation of telomerase genes expression and telomere shortening | Carrillo, Jaime CSIC; Calvete, Oriol; Pintado-Berninches, Laura CSIC ORCID ; Manguan-García, Cristina CSIC ORCID; Sevilla Navarro, Julian; Arias-Salgado, Elena G.; Sastre, Leandro CSIC ORCID; Guenechea, Guillermo; López Granados, Eduardo; Villartay, Jean-Pierre de; Revy, Patrick; Benítez, Javier; Perona Abellón, Rosario CSIC ORCID | artículo |