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openAccessAllelic-Interference-in-Prion-Replication-Is-Modulated.pdf.jpg16-mar-2021Allelic Interference in Prion Replication Is Modulated by the Convertibility of the Interfering PrPC and Other Host-Specific FactorsEspinosa Martín, Juan Carlos; Andréoletti, Olivier; Marín-Moreno, Alba; Lugan, Séverine; Aguilar-Calvo, Patricia; Cassard, Hervé; Lorenzo, Patricia ; Douet, Jean-Yves; Villa Díaz, Ana; Aron, Naima; Prieto, Irene; Huor, Alvina; Torres, Juan Maríaartículo
openAccessAn_optimized_Western_blot_assay_provides.pdf.jpg2-feb-2023An optimized Western blot assay provides a comprehensive assessment of the physiological endoproteolytic processing of the prion proteinVanni, Ilaria; Iacobone, Floriana; D'Agostino, Claudia; Giovannelli, Matteo; Pirisinu, Laura; Altmeppen, Hermann Clemens; Castilla, Joaquín; Torres, Juan María; Agrimi, Umberto; Nonno, Romoloartículo
openAccessBona-fide-atypical-scrapie-faithfully.pdf.jpg13-dic-2022Bona fide atypical scrapie faithfully reproduced for the first time in a rodent modelVidal, Enric; Sánchez-Martín, Manuel Adolfo; Eraña, Hasier; Lázaro, Sonia Pérez; Pérez-Castro, Miguel A.; Otero, Alicia; Charco, Jorge M.; Marín, Belén; López-Moreno, Rafael; Díaz-Domínguez, Carlos M.; Geijo, Mariví; Ordóñez, Montserrat; Cantero, Guillermo; di Bari, Michele; Lorenzo, Nuria L.; Pirisinu, Laura; D'Agostino, Claudia; Torres, Juan María; Béringue, V.; Telling, Glenn; Badiola, Juan J.; Pumarola, Martí; Bolea, Rosa; Nonno, Romolo; Requena, Jesús R.; Castilla, Joaquínartículo
openAccessCanine-D163-PrP-polymorphic-variant-does-not-provide.pdf.jpg12-jul-2021Canine D163-PrP polymorphic variant does not provide complete protection against prion infection in small ruminant PrP contextMarín-Moreno, Alba; Espinosa Martín, Juan Carlos; Aguilar-Calvo, Patricia; Fernández-Borges, N.; Pitarch, José Luis; González, Lorenzo; Torres, Juan Maríaartículo
closedAccessaccesoRestringido.pdf.jpg2013Cellular prion protein modulates β-amyloid deposition in aged APP/PS1 transgenic miceOrdóñez-Gutiérrez, Lara CSIC ORCID; Torres, Juan María; Gavín, Rosalina; Antón Pérez, Marta; Arroba, Ana I. CSIC ORCID; Vergara, Cristina; Río, José Antonio del; Wandosell, Francisco CSIC ORCID artículo
openAccess2215.pdf.jpg2011Central nervous system gene expression changes in a transgenic mouse model for bovine spongiform encephalopathyTortosa, R.; Castells, X.; Vidal, Elena A.; Costa, Carme; Ruiz de Villa, M.; Sánchez, Alex; Barcelá, A.; Torres, Juan María; Pumarola, Martí; Ariño, J.artículo
openAccessCharacterization_of_goat_prions.pdf.jpg8-ene-2020Characterization of goat prions demonstrates geographical variation of scrapie strains in Europe and reveals the composite nature of prion strainsNonno, Romolo; Marín-Moreno, Alba; Espinosa Martín, Juan Carlos; Fast, C.; Van Keulen, Lucien; Spiropoulos, J.; Lantier, Isabelle; Andréoletti, Olivier; Pirisinu, Laura; di Bari, Michele; Aguilar-Calvo, Patricia; Sklaviadis, T.; Papasavva-Stylianou, Penelope; Acutis, Pier Luigi; Acin, Cristina; Bossers, A.; Jacobs, Jorge G.; Vaccari, Gabriel; D'Agostino, Claudia; Chiappini, Barbara; Lantier, Frederic; Groschup, M. H.; Agrimi, Umberto; Torres, Juan María; Langeveld, J.artículo
openAccessClassical-BSE-prions-emerge-from-asymptomatic.pdf.jpg31-ago-2021Classical BSE prions emerge from asymptomatic pigs challenged with atypical/Nor98 scrapieMarín, Belén; Otero, Alicia; Lugan, Séverine; Espinosa Martín, Juan Carlos; Marín-Moreno, Alba; Vidal, Enric; Hedman, Carlos; Romero, Antonio CSIC ORCID; Pumarola, Martí; Badiola, Juan J.; Torres, Juan María; Andréoletti, Olivier; Bolea, Rosaartículo
openAccessClassical-scrapie-in-small-ruminants.pdf.jpg15-abr-2021Classical scrapie in small ruminants is caused by at least four different prion strainsMarín-Moreno, Alba; Aguilar-Calvo, Patricia; Espinosa Martín, Juan Carlos; Zamora-Ceballos, María; Pitarch, José Luis; Fernández-Borges, N.; Orge, Leonor; Andréoletti, Olivier; Nonno, Romolo; Torres, Juan Maríaartículo
openAccessCorrelation_between_Bioassay.pdf.jpgfeb-2020Correlation between bioassay and protein misfolding cyclic amplification for variant creutzfeldt-jakob disease decontamination studiesBélondrade, Maxime; Jas-Duval, Christelle; Nicot, Simon; Bruyère-Ostells, Lilian; Mayran, Charly; Herzog, L.; Reine, F.; Torres, Juan María; Fournier-Wirth, Chantal; Béringue, V.; Lehmann, Sylvain; Bougard, Daisyartículo
closedAccessoficial.pdf.jpg1-abr-2020Crossing Species Barriers Relies on Structurally Distinct Prion Assemblies and Their ComplementationIgel-Egalon, Angélique; Laferrière, Florent; Tixador, Philippe; Moudjou, Mohammed; Herzog, L.; Reine, F.; Torres, Juan María; Laude, H.; Rezaei, H. R.; Béringue, V.artículo
closedAccessoficial.pdf.jpg2-mar-2020Erratum to: Porcine Prion Protein as a Paradigm of Limited Susceptibility to Prion Strain PropagationEspinosa Martín, Juan Carlos; Marín-Moreno, Alba; Aguilar-Calvo, Patricia; Benestad, Sylvie L.; Andréoletti, Olivier; Torres, Juan Maríacorrigenda
openAccessExperimental_transmission_of_ovine.pdf.jpg20-oct-2023Experimental transmission of ovine atypical scrapie to cattleKonold, T.; Spiropoulos, J.; Hills, Janet; Abdul, Hasina; Cawthraw, S.; Phelan, Laura; McKenna, Amy; Read, Lauren; Canoyra, Sara; Marín-Moreno, Alba; Torres, Juan Maríaartículo
openAccessGlycans-not-necessary.pdf.jpg7-oct-2022Glycans are not necessary to maintain the pathobiological features of bovine spongiform encephalopathyOtero, Alicia; Barrio, Tomás; Eraña, Hasier; Charco, Jorge M.; Betancor, Marina; Díaz-Domínguez, Carlos M.; Marín, Belén; Andréoletti, Olivier; Torres, Juan María; Kong, Qingzhong; Badiola, Juan J.; Bolea, Rosa; Castilla, Joaquínartículo
closedAccessaccesoRestringido.pdf.jpg2006Group I mGluR signaling in BSE-infected bovine-PrP transgenic miceRodríguez, Agustín; Martín, Mairena; Albasanz, José Luis; Barrachina, Marta; Espinosa, Juan Carlos CSIC ORCID; Torres, Juan María; Ferrer, Isidroartículo
openAccessHomozygous-R136S-mutation-in-PRNP-gene-causes-inherited-early.pdf.jpg18-oct-2021Homozygous R136S mutation in PRNP gene causes inherited early onset prion diseaseXimelis, Teresa; Marín-Moreno, Alba; Espinosa Martín, Juan Carlos; Eraña, Hasier; Charco, Jorge M.; Hernández, Isabel; Riveira, Carmen; Alcolea, Daniel; González-Roca, Eva; Aldecoa, Iban; Molina-Porcel, Laura; Parchi, Piero; Rossi, Marcello; Castilla, Joaquín; Ruiz-García, Raquel; Gelpi, Ellen; Torres, Juan María; Sánchez-Valle, Raquelartículo
openAccessMet166-Glu168-residues-in-human-PrP-β2-α2-loop.pdf.jpg2021Met166 -Glu168 residues in human PrP β2-α2 loop account for evolutionary resistance to prion infectionEspinosa Martín, Juan Carlos; Marín-Moreno, Alba; Aguilar-Calvo, Patricia; Torres, Juan Maríaartículo
openAccessMicroRNA_Alterations_in_a_Tg501.pdf.jpg15-jun-2020MicroRNA Alterations in a Tg501 Mouse Model of Prion DiseaseToivonen, Janne Markus; Sánz-Rubio, David; López-Pérez, Óscar; Marín-Moreno, Alba; Bolea, Rosa; Osta, Rosario; Badiola, Juan J.; Zaragoza, P.; Espinosa Martín, Juan Carlos; Torres, Juan María; Martín-Burriel, Inmaculadaartículo
openAccessMixtures_of_prion_substrains.pdf.jpg19-mar-2020Mixtures of prion substrains in natural scrapie cases revealed by ovinised murine modelsBarrio, Tomás; Filali, Hicham; Otero, Alicia; Sheleby-Elías, Jessica; Marín, Belén; Vidal, Enric; Béringue, V.; Torres, Juan María; Groschup, M. H.; Andréoletti, Olivier; Badiola, Juan J.; Bolea, Rosaartículo
openAccessPorcine-Prion-Protein-as-a-Paradigm.pdf.jpg15-mar-2021Porcine Prion Protein as a Paradigm of Limited Susceptibility to Prion Strain PropagationEspinosa Martín, Juan Carlos; Marín-Moreno, Alba; Aguilar-Calvo, Patricia; Benestad, Sylvie L.; Andréoletti, Olivier; Torres, Juan Maríaartículo