Rights | Preview | Issue Date | Title | Author(s) | Type |
openAccess |  | 13-Apr-2007 | A Novel Two-domain Architecture Within the Amino Acid Kinase Enzyme Family Revealed by the Crystal Structure of Escherichia coli Glutamate 5-kinase | Marco-Marín, Clara CSIC ORCID; Gil-Ortiz, Fernando CSIC ORCID; Pérez-Arellano, Isabel CSIC; Cervera, Javier; Fita, Ignacio CSIC ORCID ; Rubio, Vicente CSIC ORCID | artículo |
openAccess |  | May-2022 | CIBERER: Spanish national network for research on rare diseases: A highly productive collaborative initiative | Luque, Juan M. CSIC; Mendes, Ingrid; Gómez, Beatriz; Morte, Beatriz CSIC ORCID; Heredia, Miguel CSIC; Lopez Herreras, Enrique; Corrochano, Virginia; Bueren, Juan; Gallano, Pia; Artuch, Rafael; Fillat, Cristina CSIC; Pérez-Jurado, Luis Alberto; Montoliu, Lluís CSIC ORCID ; Carracedo, Ángel; Millán, José María; Webb, Susan M.; Palau, Francesc; CIBERER Network; Lapunzina, Pablo; Albiñana, Virginia CSIC; Arjona, Emilia CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID ; Botella, Luisa María CSIC ORCID ; Pinto, Sheila CSIC; Rodríguez de Córdoba, Santiago ; Ruiz, Ángela; Antiñolo, Guillermo CSIC ORCID; Borrego, Salud CSIC ORCID; Bravo-Gil, Nereida CSIC; González-del Pozo, María; Méndez-Vidal, Cristina CSIC ORCID; Arbones, Maria L. CSIC ORCID ; Caparrós-Martín, José Antonio; Cediel, Rafael CSIC; Contreras, Julio CSIC; Estañ, María Cristina CSIC; Guerrero-López, Rosa CSIC; Jiménez-Estrada, Juan Andrés CSIC; Manguan-García, Cristina CSIC ORCID; Murillo-Cuesta, Silvia CSIC ORCID; Palencia-Campos, Adrián CSIC; Perona Abellón, Rosario CSIC ORCID; Rivera-Barahona, Ana CSIC; Rodriguez-de la Rosa, Lourdes CSIC ORCID; Ruiz-Pérez, Victor L. CSIC ORCID; Sastre, Leandro CSIC ORCID; Valencia, María CSIC; Varela-Nieto, Isabel CSIC ORCID ; Cervera, Javier; Cima, Sergio de CSIC ORCID; Gougeard, Nadine CSIC ORCID; Heredia, Miguel CSIC; Llácer, José Luis CSIC ORCID ; Marco-Marín, Clara CSIC ORCID; Marina, Alberto CSIC ORCID ; Mollá, Belén CSIC ORCID; Moreno-Estellés, Mireia CSIC ORCID; Pérez-Jiménez, Eva CSIC ORCID; Rubio, Vicente CSIC ORCID ; Sanz, Pascual CSIC ORCID ; Cortés-Rodríguez, Ana; Navas, Plácido CSIC ORCID; Sánchez Cuesta, Ana María; Santos-Ocaña, Carlos CSIC ORCID ; Fraga, Mario F. CSIC ORCID; Nieto, M. Ángela CSIC ORCID | artículo de revisión |
closedAccess |  | 11-Sep-2014 | Crystal structures of human carbamoyl phosphate synthetase 1 (CPS1) shed light on domains functions, substrate tunnels and allosteric activation, and allow rationalization of inborn CPS1 deficiency | Cima, Sergio de CSIC ORCID; Polo, Luis Mariano CSIC ORCID; Díez-Fernández, Carmen CSIC; Cervera, Javier; Fita, Ignacio CSIC ORCID ; Rubio, Vicente CSIC ORCID | póster de congreso |
closedAccess |  | 6-Sep-2016 | Deciphering carbamoyl phosphate synthetase (CPS1) deficiency and urea cycle regulation by determining the structures of human CPS1 in the absence and in the presence of N-acetyl-L-glutamate. | Cima, Sergio de CSIC ORCID; Polo, Luis Mariano CSIC ORCID; Díez-Fernández, Carmen CSIC; Martínez, Ana I.; Cervera, Javier; Fita, Ignacio CSIC ORCID ; Rubio, Vicente CSIC ORCID | póster de congreso |
closedAccess |  | 19-Jul-2014 | Human carbamoyl phosphate synthetase: structure, function and pathology | Rubio, Vicente CSIC ORCID ; Cima, Sergio de CSIC ORCID; Polo, Luis Mariano CSIC ORCID; Díez-Fernández, Carmen CSIC; Cervera, Javier; Fita, Ignacio CSIC ORCID | comunicación de congreso |
closedAccess |  | 27-Aug-2014 | Looking at Metabolic Regulation and Inborn Errors from a Structural Viewpoint: a Urea Cycle Example | Cima, Sergio de CSIC ORCID; Polo, Luis Mariano CSIC ORCID; Díez-Fernández, Carmen CSIC; Cervera, Javier; Fita, Ignacio CSIC ORCID ; Rubio, Vicente CSIC ORCID | comunicación de congreso |
openAccess |  | 23-Nov-2015 | Structure of human carbamoyl phosphate synthetase: deciphering the on/off switch of human ureagenesis | Cima, Sergio de CSIC ORCID; Polo, Luis Mariano CSIC ORCID; Díez-Fernández, Carmen CSIC; Martínez, Ana I.; Cervera, Javier; Fita, Ignacio CSIC ORCID ; Rubio, Vicente CSIC ORCID | artículo |
openAccess |  | 10-Oct-2018 | Structures of collagen IV globular domains: insight into associated pathologies, folding and network assembly | Casino, Patricia CSIC ORCID; Gozalbo-Rovira, Roberto CSIC ORCID ; Rodríguez-Díaz, Jesús; Banerjee, Sreedatta; Boutaud, Ariel; Rubio, Vicente CSIC ORCID ; Hudson, Billy G.; Saus, Juan; Cervera, Javier; Marina, Alberto CSIC ORCID | artículo |
openAccess |  | 20-May-2015 | The Study of Carbamoyl Phosphate Synthetase 1 Deficiency Sheds Light on the Mechanism for Switching On/Off the Urea Cycle | Díez-Fernández, Carmen CSIC; Gallego, José; Häberle, Johannes; Cervera, Javier; Rubio, Vicente CSIC ORCID | artículo |
openAccess | | Mar-2010 | Tumor suppressor p27Kip1 undergoes endolysosomal degradation through its interaction with sorting nexin 6 | Fuster, José J. CSIC ORCID; González, José María; Edo, María Dolores; Viana, Rosa CSIC ORCID ; Boya, Patricia CSIC ORCID ; Cervera, Javier; Verges, Marcel; Rivera, José; Andrés, Vicente CSIC ORCID | artículo |
openAccess |  | 18-Apr-2014 | Understanding carbamoyl phosphate synthetase (CPS1) deficiency by using the recombinantly purified human enzyme: effects of CPS1 mutations that concentrate in a central domain of unknown function | Díez-Fernández, Carmen CSIC; Hu, Liyan; Cervera, Javier; Häberle, Johannes; Rubio, Vicente CSIC ORCID | artículo |