Rights | Preview | Issue Date | Title | Author(s) | Type |
openAccess |  | 2017 | ADCK2 deficiency reduces weight gain and increases body temperature of mice in high fat diet | Hernández-Camacho, Juan Diego; Cascajo Almenara, M. V. CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Navas, Plácido CSIC ORCID | póster de congreso |
openAccess |  | 2019 | ADCK2 Haploinsufficiency Reduces Mitochondrial Lipid Oxidation and Causes Myopathy Associated with CoQ Deficiency | Vázquez-Fonseca, Luis; Schäefer, Jochen; Navas-Enamorado, Ignacio CSIC; Santos-Ocaña, Carlos CSIC ORCID ; Hernández-Camacho, Juan Diego; Guerra, Ignacio CSIC; Cascajo Almenara, M. V. CSIC ORCID; Sánchez-Cuesta, Ana CSIC ORCID; Horvath, Zoltan; Siendones, Emilio CSIC; Jou, Cristina; Casado, Mercedes; Gutierrez-Rios, Purificacion CSIC; Brea-Calvo, Gloria CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Fernández-Ayala, Daniel J. M.; Cortés-Rodríguez, Ana Belén CSIC ORCID; Rodríguez-Aguilera, Juan Carlos CSIC ORCID; Matté, Cristiane; Ribes, Antonia; Prieto-Soler, Sandra Y.; Dominguez-del-Toro, Eduardo; Francesco, Andrea Di; Aon, Miguel A.; Bernier, Michel; Salviati, Leonardo; Artuch, Rafael; Cabo, Rafael de; Jackson, Sandra; Navas, Plácido CSIC ORCID | artículo |
openAccess |  | 30-Jun-2008 | Astaxanthin from crayfish (Procambarus clarkii) as a pigmentary ingredient in the feed of laying hens | Pérez Gálvez, Antonio CSIC ORCID ; Mínguez Mosquera, María Isabel CSIC; Negro, Juan J. CSIC ORCID; Garrido Fernández, J. CSIC ORCID ; Cascajo Almenara, M. V. CSIC ORCID | artículo |
openAccess |  | 2006 | Calorie restriction induces mitochondrial biogenesis and bioenergetic efficiency | López-Lluch, Guillermo CSIC ORCID CVN ; Hunt, N.; Jones, B.; Zhu, M.; Jamieson, Hamish A.; Hilmer, S.; Cascajo Almenara, M. V. CSIC ORCID; Allard, J.; Ingram, Donald K.; Navas, Plácido CSIC ORCID; Cabo, Rafael de | artículo |
closedAccess |  | 2018 | Cardiac and placental mitochondrial characterization in a rabbit model of intrauterine growth restriction | Guitart-Mampel, M.; Gonzalez-Tendero, A.; Niñerola, S.; Morén, C.; Catalán-García, Marc; González-Casacuberta, I.; Juárez-Flores, D.L.; Ugarteburu, O.; Matalonga, L.; Cascajo Almenara, M. V. CSIC ORCID; Tort, Frederic; Cortés, Ana; Tobias, E.; Milisenda, J.C.; Grau, J. M.; Crispi, Fátima; Gratacós, Eduard; Garrabou, G.; Cardellach, F. | artículo |
openAccess |  | 2021 | Cellular models for primary coq deficiency pathogenesis study | Santos-Ocaña, Carlos CSIC ORCID ; Cascajo Almenara, M. V. CSIC ORCID; Alcázar-Fabra, María CSIC ORCID; Staiano, Carmine; López-Lluch, Guillermo CSIC ORCID CVN ; Brea-Calvo, Gloria CSIC ORCID; Navas, Plácido CSIC ORCID | artículo |
closedAccess |  | 2012 | Coenzyme Q biosynthesis is regulated by RNA-protein interaction | Cascajo Almenara, M. V. CSIC ORCID; Siendones, Emilio CSIC; Willers, Imke M. CSIC; Cuezva, José M. CSIC ORCID; Navas, Plácido CSIC ORCID | póster de congreso |
closedAccess |  | 2017 | Genetic rescue of mitochondrial and skeletal muscle impairment in an induced pluripotent stem cells model of coenzyme Q10 deficiency | Romero-Moya, Damià; Santos-Ocaña, Carlos CSIC ORCID ; Castaño, Justo P.; Rodríguez-Gómez, José A. CSIC ORCID; González-Rodríguez, Patricia CSIC ORCID; Fernández-Ayala, Daniel J. M.; Cascajo Almenara, M. V. CSIC ORCID; Montero, Raquel; Yubero, Delia; López-Barneo, José CSIC ORCID; Muñoz-Cánoves, Pura; Artuch, Rafael; Navas, Plácido CSIC ORCID; Menéndez, Pablo | artículo |
closedAccess |  | Nov-2020 | Laboratory Diagnosis of a Case with Coenzyme Q10 Deficiency | Paredes-Fuentes, Abraham J.; Juliá-Palacios, Natalia; Yubero, Delia; Cascajo Almenara, M. V. CSIC ORCID; García-Cazorla, Angels; Santos-Ocaña, Carlos CSIC ORCID ; Artuch, Rafael | artículo |
closedAccess |  | 2014 | Membrane-bound CYB5R3 is a common effector of nutritional and oxidative stress response through FOXO3a and Nrf2 | Siendones, Emilio CSIC; Santa-Cruz Calvo, Sara; Martín-Montalvo, Alejandro CSIC ORCID; Cascajo Almenara, M. V. CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Villalba, José M.; Cabo, Rafael de; Navas, Plácido CSIC ORCID | artículo |
openAccess |  | 2020 | Regulation of synthesis of coenzyme Q10 | Cascajo Almenara, M. V. CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN | capítulo de libro |
openAccess |  | 2016 | RNA-binding proteins regulate cell respiration and coenzyme Q biosynthesis by post-transcriptional regulation of COQ7 | Cascajo Almenara, M. V. CSIC ORCID; Fernández-Ayala, Daniel J. M.; Willers, Imke M. CSIC; Brea-Calvo, Gloria CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Valenzuela-Villatoro, Marina CSIC; Cuezva, José M. CSIC ORCID; Siendones, Emilio CSIC; Navas, Plácido CSIC ORCID | artículo |
closedAccess |  | 2016 | Secondary coenzyme Q10 deficiencies in oxidative phosphorylation (OXPHOS) and non-OXPHOS disorders | Yubero, Delia; Montero, Raquel; Martín, Miguel A.; Rodríguez-Aguilera, Juan Carlos CSIC ORCID; Navas, Plácido CSIC ORCID; Artuch, Rafael; García-Cazorla, Angels; Rivas Infante, Eloy; Cascajo Almenara, M. V. CSIC ORCID; Alcázar-Fabra, María CSIC ORCID; Brea-Calvo, Gloria CSIC ORCID | artículo |
closedAccess |  | Jul-2021 | Secondary CoQ10 deficiency, bioenergetics unbalance in disease and aging | Navas, Plácido CSIC ORCID; Cascajo Almenara, M. V. CSIC ORCID; Alcázar-Fabra, María CSIC ORCID; Hernández-Camacho, Juan Diego; Sánchez-Cuesta, Ana CSIC ORCID; Cortés-Rodríguez, Ana Belén CSIC ORCID; Ballesteros, Manuel CSIC ORCID; Arroyo, Antonio CSIC ORCID; Rodríguez-Aguilera, Juan Carlos CSIC ORCID; Fernández-Ayala, Daniel J. M.; Brea-Calvo, Gloria CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Santos-Ocaña, Carlos CSIC ORCID | artículo de revisión |
openAccess |  | 2013 | Survival transcriptome in the coenzyme Q10 deficiency syndrome is acquired by epigenetic modifications: a modelling study for human coenzyme Q10 deficiencies | Fernández-Ayala, Daniel J. M.; Guerra, Ignacio CSIC; Jiménez-Gancedo, Sandra CSIC; Cascajo Almenara, M. V. CSIC ORCID; Gavilán, Angela; DiMauro, Salvatore; Hirano, Michio; Briones, Paz CSIC; Artuch, Rafael; Cabo, Rafael de; Salviati, Leonardo; Navas, Plácido CSIC ORCID | artículo |
closedAccess | | 2007 | The two faces of a same function: pro- and antiapoptotic role of ubiquinone | Siendones, Emilio CSIC; Brea-Calvo, Gloria CSIC ORCID; Cascajo Almenara, M. V. CSIC ORCID; López-Lluch, Guillermo CSIC ORCID CVN ; Sánchez-Alcázar, José Antonio CSIC ORCID ; Navas, Plácido CSIC ORCID | capítulo de libro |