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openAccessScientific Reports_Aguado_2019.pdf.jpg15-Aug-201911PS04 is a new chemical entity identified by microRNA-based biosensing with promising therapeutic potential against cancer stem cellsAguado, Tania; Romero-Revilla, José A.; Granados, R.; Campuzano, Susana CSIC ORCID; Torrente-Rodríguez, Rebeca M.; Cuesta, Ángel M. ; Albiñana, Virginia CSIC; Botella, Luisa María CSIC ORCID ; Santamaría, Silvia CSIC ORCID; García-Sanz, José A. CSIC ORCID ; Pingarrón, José Manuel; Sánchez-Sancho, Francisco CSIC; Sánchez-Puelles, José María CSIC ORCID artículo
openAccess1750-1172-6-85-S1.TIFF.jpg22-Dec-20115'UTR mutations of ENG cause Hereditary Hemorrhagic TelangiectasiaDamjanovich, Kristy; Langa, Carmen CSIC; Blanco, Francisco J. CSIC ORCID ; McDonald, Jamie; Botella, Luisa María CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID ; Wooderchak-Donahue, Whitney; Stevenson, David A.; Bayrak-Toydemir, Pinarartículo
closedAccessaccesoRestringido.pdf.jpg2004A Cross-Talk between Hypoxia and TGF-β Orchestrates Erythropoietin Gene Regulation Through SP1 and SmadsSánchez-Elsner, Tilman; Ramírez, José Ramón; Rodriguez-Sanz, Francisco; Varela, Elisa; Bernabéu, Carmelo CSIC ORCID ; Botella, Luisa María CSIC ORCID artículo
openAccessjcm-11-03053.pdf.jpg28-May-2022A Novel Splicing Mutation in the ACVRL1/ALK1 Gene as a Cause of HHT2Errasti, Suriel; Peñalva, Mercedes; Recio-Poveda, Lucía ; Vilches, Susana; Casado-Vela, Juan CSIC ORCID CVN; Pérez Pérez, Julián; Botella, Luisa María CSIC ORCID ; Albiñana, Virginia CSIC; Cuesta, Ángel M. artículo
closedAccessrestringido.pdf.jpg4-Jul-2010A review on clinical management and pharmacological therapy on hereditary haemorrhagic telangiectasia (HHT)Zarrabeitia, Roberto; Albiñana, Virginia CSIC; Salcedo, Matilde; Señaris-Gonzalez, B.; Fernandez-Forcelledo, José L.; Botella, Luisa María CSIC ORCID artículo
closedAccessaccesoRestringido.pdf.jpgJun-2015Atorvastatin-induced endothelial nitric oxide synthase expression in endothelial cells is mediated by endoglinZemankova, L.; Varejckova, Michala; Dolezelova, Eva; Fikrova, Petra; Jezkova, Katerina; Rathouska, Jana; Červený, Lukáš; Botella, Luisa María CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID ; Nachtigal, Petrartículo
openAccess28-Jan-2016Bazedoxifene, a new orphan drug for the treatment of bleeding in hereditary haemorrhagic telangiectasiaZarrabeitia, Roberto; Ojeda-Fernández, María Luisa CSIC; Recio-Poveda, Lucía ; Bernabéu, Carmelo CSIC ORCID ; Parra, José A.; Albiñana, Virginia CSIC; Botella, Luisa María CSIC ORCID artículo
openAccessijms_Albiñana_2022.pdf.jpg25-Jan-2022Blockade of β2-adrenergic receptor reduces inflammation and oxidative stress in clear cell renal cell carcinomaAlbiñana, Virginia CSIC; Recio-Poveda, Lucía ; González-Peramato, Pilar; Martínez-Piñeiro, Luis; Botella, Luisa María CSIC ORCID ; Cuesta, Ángel M. artículo
closedAccessaccesoRestringido.pdf.jpg1-Nov-2005Blood outgrowth endothelial cells from Hereditary Haemorrhagic Telangiectasia patients reveal abnormalities compatible with vascular lesionsFernandez-Lopez, Africa CSIC; Sanz-Rodríguez, Francisco CSIC ORCID; Zarrabeitia, Roberto; Pérez-Molino, Alfonso; Hebbeld, Robert P.; Nguyen, Julia; Bernabéu, Carmelo CSIC ORCID ; Botella, Luisa María CSIC ORCID artículo
closedAccessaccesoRestringido.pdf.jpg5-Sep-2013BMP9 mutations cause a vascular-anomaly syndrome with phenotypic overlap with hereditary hemorrhagic telangiectasiaWooderchak-Donahue, Whitney; McDonald, Jamie; O'Fallon, Brendan D.; Upton, Paul D.; Li, Wei; Roman, Beth L.; Young, Sarah; Plant, Parker; Fülöp, Gyula T.; Langa, Carmen CSIC; Morrell, Nicholas W.; Botella, Luisa María CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID ; Stevenson, David A.; Runo, James R.; Bayrak-Toydemir, Pinarartículo
openAccessF1000 Research_2017_Luisa-Maria_Botella.pdf.jpg4-Dec-2017Case Report: Propranolol increases the therapeutic response to temozolomide in a patient with metastatic paraganglioma [version 1; referees: awaiting peer review]Díaz-Castellanos, Miguel-Ángel; Villar Gómez de las Heras, Karina; Díaz-Redondo, Tamara; González-Flores, Encarnación; Albiñana, Virginia CSIC; Botella, Luisa María CSIC ORCID artículo
openAccessJ. Biol. Chem.-1997-López-Rodr__guez-29120-6-1.pdf.jpg14-Nov-1997CCAAT-enhancer-binding proteins (C/EBP) regulate the tissue specific activity of the CD11c integrin gene promoter through functional interactions with Sp1 proteinsLópez-Rodríguez, Cristina; Botella, Luisa María CSIC ORCID ; Corbí, Angel L. artículo
openAccesschicken_endoglin_Rossi.pdf.jpg2012Characterization of chicken endoglin, a member of the zona pellucida family of proteins, and its tissue expressionRossi, Elisa; Langa, Carmen CSIC; Gilsanz, Álvaro; Blanco, Francisco J. CSIC ORCID ; Ayllón, Juan; Villar, Enrique; Botella, Luisa María CSIC ORCID ; Cabañas, Carlos CSIC ORCID ; Shaw, Marlene; Bernabéu, Carmelo CSIC ORCID artículo
openAccess1471-2199-11-51.pdf.jpg29-Jun-2010Characterization of the human Activin-A receptor type II-like kinase 1 (ACVRL1) promoter and its regulation by Sp1Garrido-Martin, Eva M. CSIC; Blanco, Francisco J. CSIC ORCID ; Fernandez-Lopez, Africa CSIC; Langa, Carmen CSIC; Botella, Luisa María CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID artículo
openAccess2022 Clin Genet 101-481.pdf.jpgMay-2022CIBERER: Spanish national network for research on rare diseases: A highly productive collaborative initiativeLuque, Juan M. CSIC; Mendes, Ingrid; Gómez, Beatriz; Morte, Beatriz CSIC ORCID; Heredia, Miguel CSIC; Lopez Herreras, Enrique; Corrochano, Virginia; Bueren, Juan; Gallano, Pia; Artuch, Rafael; Fillat, Cristina; Pérez-Jurado, Luis Alberto; Montoliu, Lluís CSIC ORCID ; Carracedo, Ángel; Millán, José María; Webb, Susan M.; Palau, Francesc; CIBERER Network; Lapunzina, Pablo; Albiñana, Virginia CSIC; Arjona, Emilia CSIC ORCID ; Bernabéu, Carmelo CSIC ORCID ; Botella, Luisa María CSIC ORCID ; Pinto, Sheila CSIC; Rodríguez de Córdoba, Santiago ; Ruiz, Ángela; Antiñolo, Guillermo CSIC ORCID; Borrego, Salud CSIC ORCID; Bravo-Gil, Nereida CSIC; González-del Pozo, María; Méndez-Vidal, Cristina CSIC ORCID; Arbones, Maria L. CSIC ORCID ; Caparrós-Martín, José Antonio; Cediel, Rafael CSIC; Contreras, Julio CSIC; Estañ, María Cristina CSIC; Guerrero-López, Rosa CSIC; Jiménez-Estrada, Juan Andrés CSIC; Manguan-García, Cristina CSIC; Murillo-Cuesta, Silvia CSIC ORCID; Palencia-Campos, Adrián CSIC; Perona Abellón, Rosario CSIC ORCID; Rivera-Barahona, Ana CSIC; Rodriguez-de la Rosa, Lourdes CSIC ORCID; Ruiz-Pérez, Victor L. CSIC ORCID; Sastre, Leandro CSIC ORCID; Valencia, María CSIC; Varela-Nieto, Isabel CSIC ORCID ; Cervera, Javier; Cima, Sergio de; Gougeard, Nadine CSIC; Heredia, Miguel CSIC; Llácer, José Luis CSIC ORCID ; Marco-Marín, Clara CSIC ORCID; Marina, Alberto CSIC ORCID ; Mollá, Belén CSIC ORCID; Moreno-Estellés, Mireia CSIC ORCID; Pérez-Jiménez, Eva; Rubio, Vicente CSIC ORCID ; Sanz, Pascual CSIC ORCID ; Cortés-Rodríguez, Ana; Navas, Plácido CSIC ORCID; Sánchez Cuesta, Ana María; Santos-Ocaña, Carlos CSIC ORCID ; Fraga, Mario F. CSIC ORCID; Nieto, M. Ángela CSIC ORCID artículo de revisión
openAccessCLN5_Rojas_Art2020.pdf.jpg2020CLN5 in heterozygosis may protect against the development of tumors in a VHL patientRojas-P, Isabel de CSIC; Albiñana, Virginia CSIC; Recio-Poveda, Lucía ; Rodriguez-Rufián, Amanda; Cuesta, Ángel M. ; Botella, Luisa María CSIC ORCID 
openAccessCA3072389A1.pdf.jpg14-Feb-2019Compounds for treating Von Hippel-Lindau diseaseBotella, Luisa María CSIC ORCID ; Albiñana, Virginia CSIC; Villar Gómez de las Heras, Karinasolicitud de patente
openAccessEP3664788A0.pdf.jpg17-Jun-2020Compounds for treating Von Hippel-Lindau diseaseBotella, Luisa María CSIC ORCID ; Albiñana, Virginia CSIC; Villar Gómez de las Heras, Karinasolicitud de patente
openAccessWO2019030151A1.pdf.jpg14-Feb-2019Compounds for treating Von Hippel-Lindau diseaseBotella, Luisa María CSIC ORCID ; Albiñana, Virginia CSIC; Villar Gómez de las Heras, Karinasolicitud de patente
openAccessUS2020323798A1.pdf.jpg15-Oct-2020Compounds for treating Von Hippel-Lindau diseaseBotella, Luisa María CSIC ORCID ; Albiñana, Virginia CSIC; Villar Gómez de las Heras, Karinasolicitud de patente