Derechos | Preview | Fecha Public. | Título | Autor(es) | Tipo |
openAccess | | 2005 | Análisis genético y funcional de la frataxina y otras proteínas mitocrondriales relacionadas con ataxias cerebelosas. | González-Cabo, Pilar CSIC ORCID | tesis doctoral |
openAccess | | 23-mar-2020 | Cofilin dysregulation alters actin turnover in frataxin-deficient neurons | Muñoz-Lasso, Diana C.; Mollá, Belén CSIC ORCID; Calap-Quintana, Pablo; García Giménez, José Luis; Pallardó, Federico V.; Palau, Francesc; González-Cabo, Pilar CSIC ORCID | artículo |
openAccess | | 7-jun-2011 | Differential Expression of PGC-1α and Metabolic Sensors Suggest Age-Dependent Induction of Mitochondrial Biogenesis in Friedreich Ataxia Fibroblasts | García-Giménez, José Luis; Gimeno, Amparo; González-Cabo, Pilar CSIC ORCID; Dasí, Francisco; Bolinches-Amorós, Arantxa CSIC; Mollá, Belén CSIC ORCID; Palau Martínez, Francesc CSIC ORCID; Pallardó, Federico V. | artículo |
openAccess | | 4-abr-2011 | Disruption of the ATP-binding cassette B7 (ABTM-1/ABCB7) induces oxidative stress and premature cell death in Caenorhabditis elegans | González-Cabo, Pilar CSIC ORCID; Bolinches-Amorós, Arantxa CSIC; Cabello, Juan CSIC ORCID; Ros, Sheila CSIC; Moreno, Sergio CSIC ORCID; Palau Martínez, Francesc CSIC ORCID; Vázquez-Manrique, Rafael P. CSIC ORCID | artículo |
openAccess | | 25-ene-2010 | Flavin Adenine Dinucleotide Rescues the Phenotype of Frataxin Deficiency | González-Cabo, Pilar CSIC ORCID; Ros, Sheila CSIC; Palau Martínez, Francesc CSIC ORCID | artículo |
openAccess | | 2016 | Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition) | Klionsky, Daniel J.; Coll, Núria S. CSIC ORCID; Aldudo, Jesús CSIC ORCID; Izquierdo, José M. CSIC ORCID ; Pantazopoulou, Areti CSIC ORCID; Oeste, Clara L. CSIC ORCID; Hilfiker, Sabine; Oliver, Francisco Javier; Gotor, Cecilia CSIC ORCID ; Pérez-Pérez, María Esther CSIC ORCID ; Mollinedo, Faustino CSIC ORCID ; Lazo, Pedro A. CSIC ORCID ; Varela-Nieto, Isabel CSIC ORCID ; Martín-Sanz, Paloma CSIC ORCID ; Valverde, Ángela M. CSIC ORCID ; Aranda, Agustín CSIC ORCID ; Orozco, Helena CSIC ORCID; Triola Guillem, Gemma CSIC ORCID; Fernández-Checa, José C. CSIC ORCID; García-Ruiz, Carmen CSIC ORCID ; González-Cabo, Pilar CSIC ORCID; Villar, Margarita CSIC ORCID; Gargini, Ricardo CSIC ORCID; Miranda-Vizuete, Antonio CSIC ORCID | artículo |
openAccess | | 13-may-2014 | Mitochondrial dysfunction induced by frataxin deficiency is associated with cellular senescence and abnormal calcium metabolism | Bolinches-Amorós, Arantxa CSIC; Mollá, Belén CSIC ORCID; Pla-Martín, David CSIC; Palau Martínez, Francesc CSIC ORCID; González-Cabo, Pilar CSIC ORCID | artículo |
openAccess | | abr-2019 | Phosphodiesterase Inhibitors Revert Axonal Dystrophy in Friedreich's Ataxia Mouse Model | Mollá, Belén CSIC ORCID; Muñoz-Lasso, Diana C.; Calap, Pablo; Fernandez-Vilata, Angel; de la Iglesia-Vaya, María; Pallardó, Federico V.; Moltó, Maria Dolores; Palau Martínez, Francesc CSIC ORCID; González-Cabo, Pilar CSIC ORCID | artículo |
openAccess | | 30-ago-2017 | Reversible Axonal Dystrophy by Calcium Modulation in Frataxin-Deficient Sensory Neurons of YG8R Mice. | Mollá, Belén CSIC ORCID; Muñoz-Lasso, Diana C.; Riveiro, Fátima CSIC; Bolinches-Amorós, Arantxa CSIC; Pallardó, Federico V.; Fernandez-Vilata, Angel; de la Iglesia-Vaya, María; Palau Martínez, Francesc CSIC ORCID; González-Cabo, Pilar CSIC ORCID | artículo |
openAccess | | 2016 | Two different pathogenic mechanisms, dying-back axonal neuropathy and pancreatic senescence, are present in the YG8R mouse model of Friedreich's ataxia | Mollá, Belén CSIC ORCID; Riveiro, Fátima CSIC; Bolinches-Amorós, Arantxa CSIC; Muñoz-Lasso, Diana C.; Palau Martínez, Francesc CSIC ORCID; González-Cabo, Pilar CSIC ORCID | artículo |