Mostrando resultados 1 a 20 de 26
Siguiente >
Derechos | Preview | Fecha Public. | Título | Autor(es) | Tipo |
openAccess | | 9-ene-2009 | 3D structure of the C3bB complex provides insights into the activation and regulation of the complement alternative pathway convertase | Torreira, Eva CSIC; Tortajada, Agustín CSIC ORCID; Montes, Tamara CSIC; Rodríguez de Córdoba, Santiago ; Llorca, Óscar CSIC ORCID | artículo |
openAccess | | 2012 | Análisis estructural y funcional de proteínas del complemento asociadas con patología. | Tortajada, Agustín CSIC ORCID | tesis doctoral |
openAccess | | 15-ago-2012 | Atypical Hemolytic Uremic Syndrome-Associated variants and autoantibodies impair binding of factor H and factor H-Related protein 1 to Pentraxin 3 | Kopp, Anne; Strobel, Stefanie; Tortajada, Agustín CSIC ORCID; Rodríguez de Córdoba, Santiago ; Sánchez-Corral, Pilar CSIC ORCID; Prohászka, Zoltán; López-Trascasa, Margarita; Józsi, Mihály | artículo |
openAccess | | jun-2013 | C3 glomerulopathy-associated CFHR1 mutation alters FHR oligomerization and complement regulation | Tortajada, Agustín CSIC ORCID; Yébenes, Hugo CSIC ORCID; Anter, Jaouad CSIC; García-Fernández, Jesús CSIC ; Martínez-Barricarte, Rubén CSIC; Llorca, Óscar CSIC ORCID; Rodríguez de Córdoba, Santiago | artículo |
closedAccess | | 1-dic-2009 | Coexistence of closed and open conformations of complement factor B in the alternative pathway C3bB(Mg2+) proconvertase | Torreira, Eva CSIC; Tortajada, Agustín CSIC ORCID; Montes, Tamara CSIC; Rodríguez de Córdoba, Santiago ; Llorca, Óscar CSIC ORCID | artículo |
openAccess | | nov-2012 | Complement dysregulation and disease: from genes and proteins to diagnostics and drugs | Rodríguez de Córdoba, Santiago ; Tortajada, Agustín CSIC ORCID; Harris, Claire L.; Morgan, B. Paul | artículo |
openAccess | | ene-2012 | Complement factor H variants I890 and L1007 while commonly associated with atypical haemolytic uremic syndrome are polymorphisms with no functional significance | Tortajada, Agustín CSIC ORCID; Pinto, Sheila CSIC; Martínez-Ara, Jorge; López-Trascasa, Margarita; Sánchez-Corral, Pilar CSIC ORCID; Rodríguez de Córdoba, Santiago | artículo |
openAccess | | feb-2018 | Complete functional characterization of disease-associated genetic variants in the complement factor H gene | Martín Merinero, Héctor CSIC ORCID; Pinto, Sheila CSIC; García-Fernández, Jesús CSIC ; Arjona, Emilia CSIC ORCID ; Tortajada, Agustín CSIC ORCID; Rodríguez de Córdoba, Santiago | artículo |
closedAccess | | ene-2018 | Factor H competitor generated by gene conversion events associates with atypical hemolytic uremic syndrome | Goicoechea de Jorge, Elena CSIC ORCID; Tortajada, Agustín CSIC ORCID; Pinto, Sheila CSIC; Gastoldi, Sara; Martín Merinero, Héctor CSIC ORCID; García-Fernández, Jesús CSIC ; Arjona, Emilia CSIC ORCID ; Cao, Mercedes; Remuzzi, Giuseppe; Noris, Marina; Rodríguez de Córdoba, Santiago | artículo |
closedAccess | | jun-2022 | Factor H-related protein 1 drives disease susceptibility and prognosis in C3 glomerulopathy | Márquez-Tirado, Bárbara; Gutiérrez-Tenorio, Josué; Tortajada, Agustín CSIC ORCID; Lucientes, Laura; Caravaca-Fontán, Fernando; Malik, T. H.; Roldán Montero, Raquel; Elías, Sandra; Saiz Gonzalez, Ana; Fernández-Juárez, Gema; Sánchez-Corral, Pilar CSIC ORCID; Pickering, Matthew C.; Praga, Manuel; Rodríguez de Córdoba, Santiago ; Goicoechea de Jorge, Elena CSIC ORCID | artículo |
openAccess | | oct-2016 | Factor H-related protein 3 (FHR-3) inhibits factor H binding to pentraxins and malondialdehyde epitopes, and activates the alternative pathway via C3b binding | Csincsi, Ádám I.; Pouw, Richard B.; Tortajada, Agustín CSIC ORCID; Rodríguez de Córdoba, Santiago ; Wouters, Diana; Józsi, Mihály | comunicación de congreso |
openAccess | | mar-2017 | Functional and structural characterization of four mouse monoclonal antibodies to complement C3 with potential therapeutic and diagnostic applications | Subías, Marta CSIC ; Yébenes, Hugo CSIC ORCID; Rodríguez-Gallego, César CSIC; Martín-Ambrosio, Adrián CSIC ; Domínguez, Mercedes; Tortajada, Agustín CSIC ORCID; Rodríguez de Córdoba, Santiago ; Llorca, Óscar CSIC ORCID | artículo |
openAccess | | 2-mar-2009 | Functional basis of protection against age-related macular degeneration conferred by a common polymorphism in complement factor B | Montes, Tamara CSIC; Tortajada, Agustín CSIC ORCID; Morgan, B. Paul; Rodríguez de Córdoba, Santiago ; Harris, Claire L. | artículo |
openAccess | | abr-2014 | Genetics of atypical hemolytic uremic syndrome (aHUS) | Rodríguez de Córdoba, Santiago ; Subías, Marta CSIC ; Pinto, Sheila CSIC; Tortajada, Agustín CSIC ORCID | artículo |
openAccess | | ene-2018 | How novel structures inform understanding of complement function | Goicoechea de Jorge, Elena CSIC ORCID; Yébenes, Hugo CSIC ORCID; Serna, Marina CSIC ORCID; Tortajada, Agustín CSIC ORCID; Llorca, Óscar CSIC ORCID; Rodríguez de Córdoba, Santiago | artículo |
openAccess | | 13-sep-2010 | Human C3 mutation reveals a mechanism of dense deposit disease pathogenesis and provides insights into complement activation and regulation | Martínez-Barricarte, Rubén CSIC; Heurich, Meike; Valdés-Cañedo, Francisco; Vázquez-Martul, Eduardo; Torreira, Eva CSIC; Montes, Tamara CSIC; Tortajada, Agustín CSIC ORCID; Pinto, Sheila CSIC; López-Trascasa, Margarita; Morgan, B. Paul; Llorca, Óscar CSIC ORCID; Harris, Claire L.; Rodríguez de Córdoba, Santiago | artículo |
closedAccess | | may-2008 | Measurement of factor H variants in plasma using variant-specific monoclonal antibodies: application to assessing risk of age-related macular degeneration | Hakobyan, Svetlana; Harris, Claire L.; Tortajada, Agustín CSIC ORCID; Goicoechea de Jorge, Elena CSIC ORCID; García-Layana, Alfredo; Fernández-Robredo, Patricia; Rodríguez de Córdoba, Santiago ; Morgan, B. Paul | artículo |
openAccess | | 16-sep-2015 | Molecular basis of factor H R1210C association with ocular and renal diseases | Recalde, Sergio; Tortajada, Agustín CSIC ORCID; Subías, Marta CSIC ; Anter, Jaouad CSIC; Pinto, Sheila CSIC; Rodríguez de Córdoba, Santiago | artículo |
openAccess | | oct-2016 | Prevalent FHR-1 mutant protein generated by gene conversion reveals crucial role of factor H polymorphisms in atypical Hemolytic Uremic Syndrome (aHUS) | Tortajada, Agustín CSIC ORCID; Pinto, Sheila CSIC; Gastoldi, Sara; García-Fernández, Jesús CSIC ; Merinero, Hector; Arjona, Emilia CSIC ORCID ; Noris, Marina; Rodríguez de Córdoba, Santiago | comunicación de congreso |
openAccess | | abr-2016 | Serum properdin consumption as a biomarker of C5 convertase dysregulation in C3 glomerulopathy | Corvillo, Fernando; Bravo García-Morato, María; Nozal, Pilar; Garrido, Sofía; Tortajada, Agustín CSIC ORCID; Rodríguez de Córdoba, Santiago ; López-Trascasa, Margarita | artículo |