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Derechos | Preview | Fecha Public. | Título | Autor(es) | Tipo |
openAccess | | dic-2018 | Intracellular cholesterol accumulation and coenzyme Q10 deficiency in Familial Hypercholesterolemia | Suarez-Rivero, Juan M. CSIC ORCID; Mata, Mario de la CSIC ORCID; Delgado Pavón, Ana CSIC; Villanueva-Paz, Marina CSIC ORCID; Povea-Cabello, Suleva; Cotán, David CSIC; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Ybot, Patricia CSIC ORCID; Salas, Joaquín J. CSIC ORCID ; Muñiz, Ovidio; Cordero, Mario de; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 1-sep-2018 | Pantothenate Rescues Iron Accumulation in Pantothenate Kinase-Associated Neurodegeneration Depending on the Type of Mutation | Álvarez-Córdoba, Mónica; Fernández-Khoury, Aida; Villanueva-Paz, Marina CSIC ORCID; Gómez-Navarro, Carmen; Villalón-García, Irene; Suarez-Rivero, Juan M. CSIC ORCID; Povea-Cabello, Suleva; Mata, Mario de la CSIC ORCID; Cotán, David CSIC; Talaverón-Rey, Marta; Salas, Joaquín J. CSIC ORCID ; Pérez-Villegas, Eva María; Díaz-Quintana, Antonio; Armengol, José A.; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | may-2019 | Pathophysiological characterization of MERRF patient-specific induced neurons generated by direct reprogramming | Villanueva-Paz, Marina CSIC ORCID; Povea-Cabello, Suleva; Villalón-García, Irene; Suarez-Rivero, Juan M. CSIC ORCID; Álvarez-Córdoba, Mónica; Mata, Mario de la CSIC ORCID; Talaverón-Rey, Marta; Jackson, Sandra; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
openAccess | | 2014 | PEGylated versus non-PEGylated magnetic nanoparticles as camptothecin delivery system | Castillo Hernández, Paula Margarita CSIC ORCID; Mata, Mario de la CSIC ORCID; Casula, María F.; Sánchez-Alcázar, José Antonio CSIC ORCID ; Zaderenko, Paula | artículo |
openAccess | | 2015 | Pharmacological Chaperones and Coenzyme Q10 Treatment Improves Mutant β-Glucocerebrosidase Activity and Mitochondrial Function in Neuronopathic Forms of Gaucher Disease | Mata, Mario de la CSIC ORCID; Cotán, David CSIC; Oropesa-Ávila, Manuel CSIC; Garrido-Maraver, Juan CSIC ORCID; Cordero, Mario D. CSIC ORCID; Villanueva-Paz, Marina CSIC ORCID; Delgado Pavón, Ana CSIC; Alcocer-Gómez, Elísabet; Lavera, I. de; Ybot, Patricia CSIC ORCID; Zaderenko, Paula; Ortiz-Mellet, Carmen; García Fernández, José Manuel CSIC ORCID; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 2012 | Recovery of MERRF Fibroblasts and Cybrids Pathophysiology by Coenzyme Q 10 | Mata, Mario de la CSIC ORCID; Garrido-Maraver, Juan CSIC ORCID; Cotán, David CSIC; Cordero, Mario D. CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Gómez Izquierdo, Lourdes; Miguel, Manuel de; Bautista Lorite, Juan; Rivas Infante, Eloy; Ybot, Patricia CSIC ORCID; Jackson, Sandra; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 19-oct-2012 | Screening of effective pharmacological treatments for MELAS syndrome using yeasts, fibroblasts and cybrid models of the disease | Garrido-Maraver, Juan CSIC ORCID; Cordero, Mario D. CSIC ORCID; Domínguez-Moñino, Irene CSIC ORCID; Pereira-Arenas, Sheila; Lechuga-Vieco, Ana V.; Cotán, David CSIC; Mata, Mario de la CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Miguel, Manuel de; Bautista Lorite, Juan; Rivas Infante, Eloy; Álvarez-Dolado, Manuel CSIC ORCID CVN; Navas, Plácido CSIC ORCID; Jackson, Sandra; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 6-may-2011 | Secondary coenzyme Q10 deficiency triggers mitochondria degradation by mitophagy in MELAS fibroblasts | Cotán, David CSIC; Cordero, Mario D. CSIC ORCID; Garrido-Maraver, Juan CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Rodríguez-Hernández, Ángeles CSIC ORCID; Gómez Izquierdo, Lourdes; Mata, Mario de la CSIC ORCID; Miguel, Manuel de; Bautista Lorite, Juan; Rivas Infante, Eloy; Jackson, Sandra; Navas, Plácido CSIC ORCID; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 2014 | Targeted delivery of pharmacological chaperones for Gaucher disease to macrophages by a mannosylated cyclodextrin carrier | Rodríguez-Lavado, Julio; Mata, Mario de la CSIC ORCID; Jiménez Blanco, José L.; García Moreno, María Isabel; Benito, Juan M. CSIC ORCID CVN ; Díaz-Quintana, Antonio; Sánchez-Alcázar, José Antonio CSIC ORCID ; Ortiz-Mellet, Carmen; García Fernández, José Manuel CSIC ORCID | artículo |
closedAccess | | 2016 | Targeting autophagy and mitophagy for mitochondrial diseases treatment | Villanueva-Paz, Marina CSIC ORCID; Cotán, David CSIC; Garrido-Maraver, Juan CSIC ORCID; Cordero, Mario D. CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Mata, Mario de la CSIC ORCID; Delgado Pavón, Ana CSIC; Lavera, I. de; Alcocer-Gómez, Elísabet; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 2016 | The connections among autophagy, inflammasome and mitochondria | Lavera, I. de; Delgado Pavón, Ana CSIC; Villanueva-Paz, Marina CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Mata, Mario de la CSIC ORCID; Alcocer-Gómez, Elísabet; Garrido-Maraver, Juan CSIC ORCID; Cotán, David CSIC; Álvarez-Córdoba, Mónica; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |
closedAccess | | 2016 | The role of autophagy and mitophagy in mitochondrial diseases | Villanueva-Paz, Marina CSIC ORCID; Cotán, David CSIC; Cordero, Mario D. CSIC ORCID; Garrido-Maraver, Juan CSIC ORCID; Oropesa-Ávila, Manuel CSIC; Mata, Mario de la CSIC ORCID; Delgado Pavón, Ana CSIC; Alcocer-Gómez, Elísabet; Lavera, I. de; Sánchez-Alcázar, José Antonio CSIC ORCID | capítulo de libro |
closedAccess | | mar-2000 | TNF-alpha but not IL-1alpha is correlated with PGE1-dependent protection against acute D-galactosamine-induced liver injury | Muntané, Jordi CSIC ORCID; Montero, J. L.; Lozano, J. M.; Miranda-Vizuete, Antonio CSIC ORCID; Mata, Mario de la CSIC ORCID; Miño, G. | artículo |
closedAccess | | 2017 | Two coffins and a funeral: early or late caspase activation determines two types of apoptosis induced by DNA damaging agents | Oropesa-Ávila, Manuel CSIC; Cruz, Patricia de la CSIC; Porcuna, Jesús; Villanueva-Paz, Marina CSIC ORCID; Fernández-Vega, Alejandro CSIC; Mata, Mario de la CSIC ORCID; Lavera, I. de; Suarez-Rivero, Juan M. CSIC ORCID; Luzón-Hidalgo, Raquel CSIC ORCID; Álvarez-Córdoba, Mónica; Cotán, David CSIC; Zaderenko, Paula; Cordero, Mario D. CSIC ORCID; Sánchez-Alcázar, José Antonio CSIC ORCID | artículo |